All lysosomal storage diseases are autosomal recessive in transmission except Hunters disease and Fabry disease which are X linked recessive.
As Hunter syndrome is X linked recessive it will only affect males.
Delineation of soft tissue structures can be made by use of contrast media with CT scan. Iodinated contrast: 1.Ionic monomers:(high osmolar contrast) Amidotriazoate,iothalamate,iothalamate 2.ionic dimers(low osmolar contrast agent) Ioxoglate 3.non ionic monomers: iohexal,iopentol,ioxilan,iomperal,iversal,iopromide,iobitridol, 4.non ionic dimers(iso osmolar contrast agents)iotrolan,iodixanol Barium contrast agents 1.barium swallow 2.barium meal follow through 3.barium enema **In tracheo oesophagial fistula and oesophagial atresia DIANOSIL **GASTROGRAFFIN is preferred in perforation peritonitis and intestinal obstruction.
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